My child, the Cyborg (or living with #chd and getting a Pacemaker)

2011-12-18 21h35_47I didn’t write much about August, and the last open heart surgery – frankly, some of it, I don’t even know how to go into.

It was both a “OMG, this is awesome!” with the successful surgery that quite quickly turned into an “OMG, this sucks.” when Jacob’s heartbeat did not regulate itself after the surgery and he had to be placed on an external pacemaker. When you start cutting into the heart, the electrical system that runs it apparently does not have a big breaker box that the surgeons can just kind of meander around and avoid. Each previous surgery, he left the operating room with pacemaker wires just in case, but never had to be hooked up to one. This time, he left with one.

Waiting for My Real Heartbeat to Begin

Our obscenely long ICU stay was due to the external pacemaker, as the box literally is just next to him and should he get up and trip and rip out the wires – well, that would be bad. He was not allowed to get up without an army of people going “Watch the wires!” as he moved from the bed to the chair and back again. We hovered over him for good measure, as well.

We waited. After heart surgery, the heart oftentimes goes back to the way it was after it gets over the shock of being cut on, and the doctors all hoped that would be the case here. The way they checked was that they would come in every morning at 6 AM on rounds, dial down the pacemaker, and see if his heart rhythm stayed steady or sunk like a stone.

Since we now have a permanent pacemaker, you can probably surmise how this went. Each and every day at 6am during rounds we would greet the day watching our child’s heart slow, the blood drain from his face, and his expression attempt to cover his horror at feeling his heart beat slow. Then, when they were convinced nothing had changed, his shock at the quick return back to the pacemaker’s induced rhythm.

It was some of the worst moments I’ve had with CHD, and CHD provides a plethora of soul-battering shock moments. Sitting there as a parent as you watch the doctors deliberately turn down your child’s heartbeat, watch how it affects him, and trying to smile and remain calm as if it is perfectly normal to watch someone turn off your child. It is a test of self-control.

The parental urge to rip their hands from that Pacemaker machine is overwhelming.

The Heart’s Electric System – awesomely reliable. Until it isn’t.

It was explained to us that the heart has it’s main electrical system, and 2 backup systems. The heart is very serious about keeping you alive – the heart is not dependent on the nervous system to pump or beat, but it is dependent upon its own specialized electrical system.

The SA Node is your main system, and is the “dominant pacemaker”, and usually fires at a rate of 60-100 times each minute. If that fails, you have the AV Junction as a back-up pacemaker, and its intrinsic firing rate is normally 40-60 each minute – slower than the SA node. Then there is a third backup system, the Purkinje network which initiates electrical impulses at a rate of 20-40 each minute – which may not produce enough cardiac output to sustain consciousness or even to sustain life.

When the doctors told us that the SA Node and the AV Junction were shot to hell and were unlikely to come back, we were stunned. Jacob had one electrical system working, and it beat so slow that it’s likely if he was taken off the Pacemaker he would simply pass out within seconds.

This was a hard bridge to cross.

After the surgery we were elated – the doctors were so impressed with the surgery that football and competitive sports were suddenly possible. Things we were unable to allow him to do for years suddenly became potentials. His heart came out of the surgery functioning better then it ever had. The future had grown bright for such a short time, and before we were even out of the hospital, it had thrown something at us again.

It was hard. That one week where I felt all luck and G-d himself were on our side was so short lived. It was like returning to that moment before CHD showed up, that time as a parent where you look down the road and you feel anything is possible.

“Dude. I’m Gonna be a Cyborg!”

Some people get pacemakers because they get a better quality of life after having it implanted. Some people get them because they are “pacemaker dependent” and cannot survive without it. My child is the latter.

It’s been an adjustment – we don’t know any Pacemaker dependent CHDers so this one’s new for us and we’re blazing the trail and adjusting on our own as best we can. Hopefully, we’ll find some eventually (hence the partial reason for this blog post).

More on the adjustment in another post.

Jen

Jen Lepp is an infuriatingly humble social media geek, a CHD Mom, and Director of Customer Service for web hosting company A Small Orange. Any and all posts, essays, opinions and so on in this blog should be assumed to be personal posts, essays, and opinions, and should not be assumed to apply to any business I work for.

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  • Mary

    I can totally relate to the horror of watching a machine run your child’s heart. My eldest daughter has had a PM since June of 2010. Sat. is our 3 yr. anniversary of suddenly finding out that she was a CHDer. It is hard to watch your child go through multiple medical procedures, and then even harder to realize this is their (and your) new reality. Do you have a Carelink for him?

  • http://www.jenlepp.com/ Jen Lepp

    Wow – how old was she when they diagnosed? We were diagnosed “late”, too, but he was 1.5 years. I’ve got a friend who was 50 before they diagnosed him, and his family mentioned “Oh, yeah, we knew about it, we didn’t think it was that big of a deal. Forgot to tell you.” after he wound up having OHS to replace his valve.

    I have a Medtronic Carelink monitor, but I haven’t logged in to the system yet – we were back so often after the surgery, pacing just checked it there. We “called the mothership” for the first time last month.

  • http://joyemullis.blogspot.com/ joye

    Mama of a pacemaker-dependent 2.5 year old here! Ethan will be 3 in March and got his pacemaker at 11 days old. We just had THE TALK with his cardiologist/EP about what activities he shouldn’t participate in. Not fun, but I guess it would be even less fun if something were to happen to those leads!

    Feel free to follow along … http://joyemullis.blogspot.com

  • Mary

    She was 8. We don’t know when she came down with it- if it was from birth or what caused it later. (We live ina rural area, so some of the drs. are great, and some of the others abilities are questionable.) She kept coming out at night after bed saying she felt weird. One night in Jan.’10, she came out again and said it felt like butterflies were trying to fly our of a tornado in her chest. I took her pulse and it was 45 bpm. I told her to lie down, and called the pediatric advice line. While on the phone with them, I took her pulse while she was lying down, and it had gone down to 40 bpm, so we got a trip to the ER without speaking to the doc. They triaged her right away, put us in the room right across from the nurses station (which I have since learned has significant meaning in the ER!), and did an EKG. The tech. left the room and the dr. came in 30 sec. later (literally), and said, ” Your daughter has a stage three heart block. We are transferring her to Stanford.” So after I called my husband to tell him, and ran home to get a few things, we found ourselves in an ambulance for a three hour ride. My other three kids were asleep the whole time. She didn’t have a PM put in right away, b/c her heart was unusually strong, but went back every two months (and went back to the ER multiple times) for 6 mths. She was scheduled for surgery the end of the summer, but her symptoms got worse, so we got a call saying, “We conferred all together, and decided she needs it now. Can you be here tomorrow?”, and she had her surgery in June. There were complications- first they could only put one lead in, and it was pacing her diaphragm, so she was having giant “hiccups” that shook her hospital bed. Then 6 hrs. later, they thought the lead had detached, and it was confirmed by x-ray. After they had her back in surgery to re-attach it, they turned on the fluoroscope, and discovered that the lead didn’t detach, it pierced her heart and her diaphragm, and was working its way out of her chest wall, so she was rushed into emergency open-heart surgery, and our overnight stay lasted 5 days. We missed our youngest daughter’s 3rd birthday, and my 14 mth. old wouldn’t have anything to do with me when we got home. We go back to the children’s hosp. 3 hrs. away every 6 mths., and use the Carelink in the alternating six months. The first time we used the Carelink, it made me queasy. I still hate it when they interrogate her pacer at the clinic. Our next appt.is in Feb.

  • http://www.jenlepp.com/ Jen Lepp

    Oh, woooow. 11 days old? I had no idea they could even put them in that young.

    And no, I know the paranoia about the leads – I swear, every “I don’t feel well” look that comes across his face totally freaks me out now. I’m having such a hard time explaining to him that he has to protect that area without scaring him.

    The other night he came into the bedroom, and said “I can feel the Pacemaker!”. This was said, of course, while he had hid fingers under the scar and he was pushing on it which, of course, made me go white and quickly snap “STOP pushing on it!”. Is it probably that easy to dislodge? Well, no. But please, can we not tempt fate, child?

    Fate kinda screws us enough occasionally all on its own.

  • http://www.jenlepp.com/ Jen Lepp

    Yeah, we did the first Carelink and are due for our second tonight. I actually didn’t think, and I don’t think my kid thought, that he would feel anything at all when we did it, but he felt “something”. Not bad, not good, but different. He could tell something was going on. It is better than the clinic, though. There’s just something so alien about the whole thing.

    Your story, though, is just horrifying – we did catch it before anything happened based on the recommendation of a peds doc that thought we should have his murmur checked out “just in case”, but it just breaks my heart how many people found this out when in the throes of a crisis you didn’t even know was coming. It was hard enough to deal with for me while he was squirmy McSquirmer baby but still relatively visibly healthy.

    And then on type of that, the issues with the pacer. Oh, man. You have my admiration for managing to stay sane.

  • http://joyemullis.blogspot.com/ joye

    Yep. First open heart surgery at 3 days, pacemaker at 11. He had an incredible surgeon, and we are very thankful for his talents!

    Ethan’s is located in his abdomen since he’s still a little guy, and he like to put his thumb behind it. When I told his cardiologist that, he told me he has patients that can flip theirs all the way over! Talk about wanting to puke.

  • Mary

    Thanks, I appreciate that :-) I don’t think I would have stayed sane without our faith and our friends.
    Our daughter is so thin that when her pacer is interrogated, it makes her have 5 hard “thumps”. and it looks like she has hiccups. She usually feels queasy after that, but mints seem to help her :-)
    I am SO glad you didn’t have to find out through crisis! Still, I’m sure it hurts to find out your child has heart disease no matter how you find out. I’m just grateful we found out, b/c our cardiologist said she could have just not woken up one morning.(shudder!) As it was, between that January and June, I didn’t sleep much. It was like having a newborn again- I checked her bpm every two hours. After we were home from having the PM implanted, after her sternum healed, I think the first time I slept through the night that year was in September!

    Are you getting some sleep now? :-D